Status Epilepticus
Content of This Page
1- Introduction
2- Causes
3- Symptoms
4- Investigations & Lab Results
5- Complications
6- Treatment
7- Prognosis
Introduction
Status Epilepticus is a life-threatening neurological emergency characterized by prolonged or repeated seizures without full recovery of consciousness between episodes. Traditionally defined as a seizure lasting more than 30 minutes, current guidelines define SE as any seizure lasting more than 5 minutes, or two or more seizures without return to baseline consciousness. It can present in various forms, with convulsive SE (generalized tonic-clonic activity) being the most common and dramatic. Non-convulsive SE is more subtle and requires EEG for diagnosis. Prompt recognition and urgent treatment are essential to prevent permanent brain injury, systemic complications, and death.

Causes
1. Neurological Causes
Epilepsy (especially medication non-compliance or withdrawal)
Stroke (ischemic or hemorrhagic)
Traumatic brain injury
Brain tumors
Central nervous system infections (e.g., meningitis, encephalitis)
2. Metabolic and Systemic Causes
Hypoglycemia or hyperglycemia
Hyponatremia or hypernatremia
Hypocalcemia, hypomagnesemia
Hepatic or renal failure
Hypoxia
3. Toxic and Drug-Related Causes
Alcohol withdrawal (especially in chronic users)
Drug overdose (e.g., theophylline, isoniazid, bupropion, cocaine)
Withdrawal from anti-seizure medications
Toxic encephalopathy
4. Infections
Sepsis
CNS infections (e.g., neurocysticercosis, HIV-related CNS disease)
5. Miscellaneous
Autoimmune encephalitis
Febrile seizures in children (progressing to SE)
Eclampsia (in pregnancy)

Symptoms
1. Convulsive Status Epilepticus (most common)
Continuous generalized tonic-clonic seizures lasting >5 minutes
Repetitive seizures without regaining consciousness between them
Loss of consciousness
Muscle rigidity and rhythmic jerking
Tongue biting, frothing, urinary incontinence
Postictal confusion or coma if seizure stops
2. Non-Convulsive Status Epilepticus
(May require EEG for diagnosis)
Altered mental status (confusion, drowsiness, agitation)
Minimal or no overt motor activity
Twitching of eyelids, facial muscles, or fingers
Speech arrest, staring, automatisms
3. Other Signs (Common to Both Types)
Autonomic instability:
Tachycardia
Hypertension or hypotension
Hyperthermia
Hypoxia
Prolonged seizure activity may lead to:
Rhabdomyolysis
Lactic acidosis
Brain injury or coma
Investigations & Lab Results
1. Immediate Bedside Tests
Capillary blood glucose: rule out hypoglycemia
Pulse oximetry and arterial blood gases (ABG): assess for hypoxia, acidosis
2. Blood Tests
Complete blood count (CBC): look for infection or anemia
Electrolytes: sodium, potassium, calcium, magnesium (correct imbalances)
Renal and liver function tests (RFT, LFT): metabolic or toxic causes
Blood glucose: hypoglycemia/hyperglycemia
Toxicology screen: drugs, alcohol, poisoning
Antiepileptic drug (AED) levels: assess compliance or toxicity
Infection markers: CRP, ESR, blood cultures if infection suspected
3. Lumbar Puncture
Indications: suspected CNS infection (e.g., meningitis, encephalitis)
Analyze for WBCs, glucose, protein, and perform cultures/PCR for viruses
4. Neuroimaging
Non-contrast CT brain (initial): rule out hemorrhage, mass, infarct
MRI brain (if stable): better for detecting encephalitis, tumors, subtle infarcts
5. Electroencephalogram (EEG)
Essential in diagnosing non-convulsive status epilepticus
Helps monitor treatment response
Continuous EEG monitoring in refractory cases
Complications
1. Neurological Complications
Permanent brain injury (especially in refractory SE)
Cognitive impairment or memory deficits
Cerebral edema
Stroke (due to prolonged hypoxia or metabolic derangement)
Chronic epilepsy or worsening seizure control
Coma or death
2. Systemic Complications
Hypoxia and respiratory failure
Aspiration pneumonia
Cardiac arrhythmias (from metabolic stress or hypoxia)
Rhabdomyolysis → acute kidney injury
Lactic acidosis and electrolyte imbalances
Hyperthermia
Hypotension or shock (especially in refractory cases)
3. Treatment-related Complications
Sedation-related respiratory depression (due to benzodiazepines or anesthetics)
Infection (e.g., from prolonged intubation or catheterization)
Hypotension from IV anesthetics (e.g., propofol, phenobarbital)
4. Mortality
Mortality rate varies (10–30%), higher in elderly or those with structural brain lesions or delayed treatment
Treatment
-Initial Stabilization (0–5 minutes)
Assess and secure airway, breathing, circulation (ABCs)
Administer oxygen and place on cardiac monitor
Establish IV access
Check capillary blood glucose and correct if hypoglycemic (e.g., 50 mL of 50% dextrose IV)
Administer thiamine 100 mg IV before glucose if alcohol use or malnutrition is suspected
Begin continuous vital sign monitoring
-First-Line Therapy (5–10 minutes)
Benzodiazepines – rapid seizure control
IV lorazepam 4 mg at 2 mg/min; may repeat once after 10–15 minutes
If no IV access:
IM midazolam 10 mg
Intranasal or buccal midazolam as alternative
-Second-Line Therapy (10–30 minutes)
Antiepileptic drugs (AEDs) – prevent recurrence
IV fosphenytoin 20 mg PE/kg (preferred due to lower risk of arrhythmias)
Alternatives:
IV phenytoin 20 mg/kg (max 50 mg/min)
IV valproic acid 20–40 mg/kg
IV levetiracetam 20–60 mg/kg
IV phenobarbital 15–20 mg/kg if others not effective
-Refractory Status Epilepticus (>30–60 minutes)
Seizures persist despite adequate benzodiazepine and AED administration
Transfer to ICU for continuous monitoring
Initiate IV anesthetic agents:
Midazolam infusion
Propofol infusion
Pentobarbital or thiopental (as last-line options)
Initiate continuous EEG monitoring
-Additional Management
Identify and treat underlying cause (e.g., infection, metabolic imbalance, trauma)
Correct electrolyte abnormalities
Maintain fluid balance and prevent complications (e.g., rhabdomyolysis, aspiration)
Monitor for drug side effects and cardiorespiratory function
Prognosis
Favorable Prognostic Factors
Prompt recognition and early treatment (within 5–10 minutes)
Young age with no underlying neurological disease
Reversible cause (e.g., metabolic, drug-related)
Good pre-morbid functional status
Short seizure duration
Generalized convulsive SE responding to initial therapy
-Poor Prognostic Factors
Delay in treatment initiation
Elderly patients or those with comorbidities
Refractory or super-refractory SE
Structural brain lesions (e.g., tumor, stroke, trauma)
Hypoxia or systemic complications (e.g., renal failure, sepsis)
Non-convulsive SE that goes unrecognized
-Outcomes
Mortality Rate:
Approximately 10–30% overall
Higher in refractory SE and in elderly patients
Neurological Sequelae:
Cognitive impairment
Motor deficits
Development of chronic epilepsy
Full recovery is possible if treated early, especially in younger patients without comorbidities or brain injury