Silicosis
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1- Definition & Types
2- Causes (Aetiology)
3- Pathophysiology
4- Clinical Features & Examination
5- Investigations
6- Management
7- Complications
8- Core Concepts
Definition & Types
Silicosis is a progressive fibrotic lung disease caused by inhaling crystalline silica dust (usually quartz), particularly in occupations involving cutting, grinding, or polishing stone.
Types:
Chronic/classic silicosis:
Most common
Appears after 10–20 years of exposure
May initially be asymptomatic
Accelerated silicosis:
5–10 years of exposure
More aggressive course
Acute silicosis (silicoproteinosis):
Within 1 year of intense exposure
Resembles alveolar proteinosis

Causes (Aetiology)
Occupational exposure in:
Mining and quarrying
Stone dressing
Pottery work
Metal grinding
Boiler scaling
Sandblasting
Pathophysiology
Inhaled silica particles are taken up by alveolar macrophages
These cause inflammatory and fibrotic responses
Leads to nodular interstitial fibrosis
Can progress to Progressive Massive Fibrosis (PMF) even after exposure stops
Increased risk of:
Tuberculosis (silicotuberculosis)
Lung cancer
COPD
Clinical Features & Examination
Type | Symptoms |
---|---|
Early/chronic silicosis | Often asymptomatic despite radiographic changes |
PMF | Cough, progressive dyspnoea, weight loss |
Acute silicosis | Rapid onset breathlessness, hypoxaemia, chest tightness |
Physical exam | May reveal fine crackles; clubbing is rare unless fibrotic |
Investigations
Imaging:
CXR:
Small, rounded nodules (3–5 mm), predominantly in upper/mid zones
May show ‘egg-shell’ calcification of hilar nodes (non-specific but suggestive)
HRCT:
Better shows nodular opacities, their conglomeration, and posterior bias (Fig 17.62)
– Lung Function:
Restrictive pattern
↓ DLCO in advanced disease
– Other:
Tuberculosis testing is essential due to increased TB risk
Autoimmune screen if connective tissue disease suspected

Management
No cure — focus is on prevention, monitoring, and symptom control
Eliminate exposure immediately — mandatory
Monitor for TB: regular screening
Symptomatic treatment:
Inhaled bronchodilators if airflow obstruction
Oxygen therapy for hypoxaemia
Pulmonary rehab
Vaccination: influenza and pneumococcus
Avoid immunosuppressants unless autoimmune overlap (e.g. Caplan’s)
Complications
Progressive massive fibrosis (PMF)
Silicotuberculosis
Lung cancer
COPD/emphysema
Possible association with renal and connective tissue diseases
Core Concepts
Silica is highly fibrogenic → disease can progress after exposure ends
Upper lobe nodules + egg-shell calcification = Think silicosis
Always exclude TB in any symptomatic patient with silicosis
Prevention is key: once fibrotic damage is done, it’s irreversible
Acute silicosis = medical emergency, mimics alveolar proteinosis