Biochemistry (Fats And Fatty Acid Metabolism Set 2)

1 / 25

Absence of phenylalanine hydroxylase
causes

A) Neonatal tyrosinemia

B) Phenylketonuria

C) Primary hyperoxaluria

D) Albinism

2 / 25

Molecular formula of cholesterol is

A) C27H45OH

B) C29H47OH

C) C29H47OH

D) C23H41OH

3 / 25

Gaucher’s disease is due to deficiency of
the enzyme:

A) Sphingomyelinase

B) Glucocerebrosidase

C) Galactocerbrosidase

D) β-Galactosidase

4 / 25

Richner-Hanhart syndrome is due to
defect in

A) Tyrosinase

B) Phenylalanine hydroxylase

C) Hepatic tyrosine transaminase

D) Fumarylacetoacetate hydrolase

5 / 25

The enzyme acyl-CoA synthase catalyses the conversion of a fatty acid of an active
fatty acid in the presence of

A) AMP

B) ADP

C) ATP

D) GTP

6 / 25

Long chain fatty acids are first activated
to acetyl-CoA in

A) Cytosol

B) Microsomes

C) Nucleus

D) Mitochondria

7 / 25

Palmitic, oleic or stearic acid ester of cholesterol used in manufacture of cosmetic creams is

A) Elaidic oil

B) Lanoline

C) Spermaceti

D) Chaulmoogric oil

8 / 25

Fucosidosis is characterized by

A) Muscle spasticity

B) Liver enlargement

C) Skin rash

D) Kidney failure

9 / 25

Amount of phenylacetic acid excreted in
the urine in phenylketonuria is

A) 100–200 mg/dL

B) 200–280 mg/dL

C) 290–550 mg/dL

D) 600–750 mg/dL

10 / 25

An important finding in Neimann-Pick
disease is

A) Leukopenia

B) Cardiac enlargement

C) Corneal opacity

D) Hepatosplenomegaly

11 / 25

Dietary fats after absorption appear in the circulation as

A) HDL

B) VLDL

C) LDL

D) Chylomicron

12 / 25

Metachromatic leukodystrophy is due to
deficiency of enzyme:

A) α-Fucosidase

B) Arylsulphatase A

C) Ceramidase

D) Hexosaminidase A

13 / 25

Neonatal tyrosinemia improves on administration of

A) Thiamin

B) Riboflavin

C) Pyridoxine

D) Ascorbic acid

14 / 25

An important finding of Fabry’s disease
is

A) Skin rash

B) Exophthalmos

C) Hemolytic anemia

D) Mental retardation

15 / 25

Long chain fatty acids penetrate the inner mitochondrial membrane

A) Freely

B) As acyl-CoA derivative

C) As carnitine derivative

D) Requiring Na dependent carrier

16 / 25

The enzymes of β-oxidation are found in

A) Mitochondria

B) Cytosol

C) Golgi apparatus

D) Nucleus

17 / 25

A significant feature of Broad Beta disease
is

A) Hypocholesterolemia

B) Hypotriacylglycerolemia

C) Absence of Apo-D

D) Abnormality of Apo-E

18 / 25

An important feature of Zellweger ’s
syndrome is

A) Hypoglycemia

B) Accumulation of phytanic acid in tissues

C) Skin eruptions

D) Accumulation of C26-C38 polyenoic acid in brain tissues

19 / 25

The cholesterol molecule is

A) Benzene derivative

B) Quinoline derivative

C) Steroid

D) Straight chain acid

20 / 25

Salkowski test is performed to detect

A) Glycerol

B) Cholesterol

C) Fatty acids

D) Vitamin D

21 / 25

Carnitine is synthesized from

A) Lysine and methionine

B) Glycine and arginine

C) Aspartate and glutamate

D) Proline and hydroxyproline

22 / 25

Free fatty acids are transported in the blood

A) Combined with albumin

B) Combined with fatty acid binding protein

C) Combined with β -lipoprotein

D) In unbound free salts

23 / 25

Plasma tyrosine level in Richner-Hanhart
syndrome is

A) 1–2 mg/dL

B) 2–3 mg/dL

C) 4–5 mg/dL

D) 8–10 mg/dL

24 / 25

Characteristic finding in Gaucher's disease is

A) Night blindness

B) Renal failure

C) Hepatosplenomegaly

D) Deafness

25 / 25

A significant feature of Tangier disease is

A) Impairment of chylomicron formation

B) Hypotriacylglycerolmia

C) Absence of Apo-C-II

D) Absence of Apo-C-I

Your score is

The average score is 40%

Fats And Fatty Acid Metabolism Set 2

Fats And Fatty Acid Metabolism Set 2

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