Fats And Fatty Acid Metabolism Set 3

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Biochemistry (Fats And Fatty Acid Metabolism Set 3)

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1. An inborn error, maple syrup urine
disease is due to deficiency of the enzyme:

A) Isovaleryl-CoAhydrogenase

B) Phenylalnine hydroxylase

C) Adenosyl transferase

D) α-Ketoacid decarboxylase

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2. Phrynoderma is a deficiency of

A) Essential fatty acids

B) Proteins

C) Amino acids

D) None of these

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3. An important feature of maple syrup
urine disease is

A) Patient can not be treated by dietary regulation

B) Without treatment death, of patient may occur by the end of second year of life

C) Blood levels of leucine, isoleucine and serine are increased

D) Excessive brain damage

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4. Tyrosinosis is due to defect in the enzyme:

A) Fumarylacetoacetate hydrolase

B) p-Hydroxyphenylpyruvate hydroxylase

C) Tyrosine transaminase

D) Tyrosine hydroxylase

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5. A characteristic feature of Kwashiorkar is

A) Fatty liver

B) Emaciation

C) Low insulin level

D) Occurrence in less than 1 year infant

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6. The deficiency of both energy and protein
causes

A) Marasmus

B) Kwashiorkar

C) Diabetes

D) Beri-beri

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7. Minimum dietary fibre is found in

A) Dried apricot

B) Peas

C) Bran

D) Cornflakes

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8. A dietary deficiency in both the quantity
and the quality of protein results in

A) Kwashiorkar

B) Marasmus

C) Xerophtalmia

D) Liver diseases

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9. A high fibre diet is associated with reduced incidence of

A) Cardiovascular disease

B) C.N.S. disease

C) Liver disease

D) Skin disease

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10. The percentage of linoleic acid in safflower oil is

A) 73

B) 57

C) 40

D) 15

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11. The percentage of polyunsaturated fatty
acids in butter is

A) 60

B) 37

C) 25

D) 3

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12. An important finding in glycinuria is

A) Excess excretion of oxalate in the urine

B) Deficiency of enzyme glycinase

C) Significantly increased serum glycine level

D) Defect in renal tubular reabsorption of glycine

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13. Dietary fibres are rich in

A) Cellulose

B) Glycogen

C) Starch

D) Proteoglycans

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14. Maple syrup urine disease becomes
evident in extra uterine life by the end of

A) First week

B) Second week

C) Third week

D) Fourth week

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15. Alkaptonuria occurs due to deficiency of
the enzyme:

A) Maleylacetoacetate isomerase

B) Homogentisate oxidase

C) p-Hydroxyphenylpyruvate hydroxylase

D) Fumarylacetoacetate hydrolase

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16. Increased urinary indole acetic acid is
diagnostic of

A) Maple syrup urine disease

B) Hartnup disease

C) Homocystinuia

D) Phenylketonuria

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17. Ochronosis is an important finding of

A) Tyrosinemia

B) Tyrosinosis

C) Alkaptonuria

D) Richner Hanhart syndrome

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18. The percentage of polyunsaturated fatty
acids in soyabean oil is

A) 62

B) 10

C) 3

D) 2

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19. Dietary fibre denotes

A) Undigested proteins

B) Plant cell components that cannot be digested by own enzymes

C) All plant cell wall components

D) All non digestible water insoluble polysaccharide

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20. Kwashiorkar is characterized by

A) Night blindness

B) Edema

C) Easy fracturability

D) Xerophthalmia

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21. An important finding in Histidinemia is

A) Impairment of conversion of α-Glutamate to α-ketoglutarate

B) Speech defect

C) Decreased urinary histidine level

D) Patients can not be treated by diet

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22. Obesity generally reflects excess intake of energy and is often associated with the
development of

A) Nervousness

B) Non-insulin dependent diabetes mellitus

C) Hepatitis

D) Colon cancer

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23. A bland diet is recommended in

A) Peptic ulcer

B) Atherosclerosis

C) Diabetes

D) Liver disease

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24. A characteristic feature of marasmus is

A) Severe hypoalbuminemia

B) Normal epinephrine level

C) Mild muscle wasting

D) Low insulin and high cortisol level

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25. In glycinuria daily urinary excretion of glycine ranges from

A) 100–200 mg

B) 300–500 mg

C) 600–1000 mg

D) 1100–1400 mg

Your score is

The average score is 4%

Fats And Fatty Acid Metabolism Set 3

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