The enzymes of β-oxidation are found in

The enzyme acyl-CoA synthase catalyses the conversion of a fatty acid of an active
fatty acid in the presence of

Salkowski test is performed to detect

Long chain fatty acids penetrate the inner mitochondrial membrane

Characteristic finding in Gaucher's disease is

A significant feature of Tangier disease is

An important finding of Fabry’s disease
is

Molecular formula of cholesterol is

A significant feature of Broad Beta disease
is

Plasma tyrosine level in Richner-Hanhart
syndrome is

An important feature of Zellweger ’s
syndrome is

Dietary fats after absorption appear in the circulation as

Gaucher’s disease is due to deficiency of
the enzyme:

Richner-Hanhart syndrome is due to
defect in

Absence of phenylalanine hydroxylase
causes

An important finding in Neimann-Pick
disease is

Neonatal tyrosinemia improves on administration of

Palmitic, oleic or stearic acid ester of cholesterol used in manufacture of cosmetic creams is

The cholesterol molecule is

Fucosidosis is characterized by

Long chain fatty acids are first activated
to acetyl-CoA in

Metachromatic leukodystrophy is due to
deficiency of enzyme:

Carnitine is synthesized from

Free fatty acids are transported in the blood

Amount of phenylacetic acid excreted in
the urine in phenylketonuria is